Clinical reasoning: seizures in a child with sensorineural deafness and agitation.

S. Auvin, MD, PhD E. Lejay, MD C. Delanoe, MD I. Denjoy, MD J.-M. Lupoglazoff, MD, PhD J.-C. Mercier, MD, PhD L. Titomanlio, MD, PhD SECTION 1 A 4-year-old girl was seen in the pediatric emergency department because of a first generalized tonic-clonic seizure that occurred at school. The seizure was preceded by a sudden, prolonged attack of unconsciousness, lasted 5 minutes, and was followed by drowsiness. The parents were first cousins of Algerian descent. She had an unremarkable family history. Pregnancy and delivery were uneventful. At age 4, she underwent bilateral cochlear implantation for congenital sensorineural deafness. Neurologic examination was notable for deafness and marked agitation, which was reported to be usual by her parents. Psychomotor development was mildly delayed.